儿茶酚胺敏感性多形性室性心动过速

摘要：儿茶酚胺敏感性多形性室速(CPVT)是一种是好发于青少年的遗传性心律失常综合征，其核心是由肾上腺素所诱发的心律紊乱。其典型的临床特征是运动或情绪激动时诱发室性心动过速，常伴发晕厥,甚至发生猝死。对于既往有晕厥或室速发作的患者，应当坚持使用β-受体阻滞剂(Ⅰa类证据)，CPVT患者发生过心脏骤停为埋藏式心脏转复除颤器(ICD)治疗的Ⅱa类适应证。

Catecholaminergic polymorphic ventricular tachycardia

??Abstract??Catecholaminergic polymorphic ventricular tachycardia (CPVT)??induced by adrenergic stress??is an inherited cardiac arrhythmia syndrome mostly found in adolescence.Patients with CPVT typically present with exercise??or emotion??induced ventricular arrhythmia leading to onset of syncope or sudden cardiac death.Beta-blockers are strongly indicated (??a) for patients with clinically??diagnosed CPVT based on the previous history??whereas intracardiac defibrillator implantation is recommended for those with CPVT who previously experienced cardiac arrest. ??????