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鞍区原发性脉络丛乳头状瘤临床病理观察
引用本文:袁峥,桂秋萍,宋欣. 鞍区原发性脉络丛乳头状瘤临床病理观察[J]. 诊断病理学杂志, 2011, 18(3): 222-225. DOI: 10.3969/j.issn.1007-8096.2011.03.018
作者姓名:袁峥  桂秋萍  宋欣
作者单位:1. 解放军总医院病理科,北京100853;中国医学科学院肿瘤医院肿瘤研究所病理科,北京100021
2. 解放军总医院病理科,北京,100853
摘    要:目的探讨鞍区原发性脉络丛乳头状瘤的临床病理特征。方法对1例原发于鞍区的脉络丛乳头状瘤的影像学、组织病理学和免疫组化特征进行研究,结合文献讨论其临床病理特征及鉴别诊断。结果磁共振成像显示蝶鞍增大,其内可见团块状肿块,侵及鞍上池;脑室系统无异常。内镜经鼻蝶入路行肿物切除术。镜下观察可见肿瘤组织类似于正常脉络丛,呈乳头状结构,由单层或假复层柱状肿瘤上皮细胞围绕纤维血管轴形成。肿瘤细胞异型性小,细胞核圆或卵圆形,位于上皮基底部。免疫组化显示肿瘤细胞CK-pan、vimtentin、EMA和TTF-1(+),而S-100蛋白、神经胶质酸性蛋白、Syn和嗜铬粒蛋白(-)。结论原发于鞍区的脉络丛乳头状瘤非常罕见,影像学易与垂体腺瘤等相混淆。明确诊断依赖于病理组织学观察及免疫组化标记。外科手术完整切除可治愈。

关 键 词:脉络丛乳头状瘤  鞍区  病理学  磁共振成像  鉴别诊断

Primary choroid plexus papilloma of sellar region:a clinicopathologic analysis
YUAN Zheng,GUI Qiu-ping,SONG Xin. Primary choroid plexus papilloma of sellar region:a clinicopathologic analysis[J]. Chinese Journal of Diagnostic Pathology, 2011, 18(3): 222-225. DOI: 10.3969/j.issn.1007-8096.2011.03.018
Authors:YUAN Zheng  GUI Qiu-ping  SONG Xin
Affiliation:YUAN Zheng1,2,GUI Qiu-ping1,SONG Xin1(1.Department of Pathology,General Hospital of Chinese PLA,Beijing 100853,China,2.Department of Pathology,Cancer Institute and Hospital,Chinese Academy of Medical Sciences,Beijing 100021,China)
Abstract:Objective To study the clinicopathological features of primary choroid plexus papillomas in the sellar region.Methods Radiographical pattern,histological observation and immunohistochemical studies were conducted in a case of primary choroid plexus papillomas of the sellar region,and its clinical findings,histopathologic features and differential diagnosis were discussed in combination with review of the literature.Results Magnetic resonance imaging demonstrated a mass in the sellar region,which occupied th...
Keywords:Choroid plexus papillomas  Sellar region  Pathology  Magnetic resonance imaging  Differential diagnosis  
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