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Fibrosarcoma in Children: A Rare Tumour with Long-Term Survival even with Advanced Disease A Report of 3 Cases |
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| Authors: | Peer K Lilleng Odd R Monge Anders Wall e Clement S Trovik Markus Hordvik Johan H ie Olav Dahl Gisle Bang |
| Institution: | a Department of Pathology, Haukeland University Hospital, Oslo, Norway b Department of Oncology, Haukeland University Hospital, Oslo, Norway c Department of Orthopedic Surgery, Haukeland University Hospital, Oslo, Norway d Department of Radiology, Haukeland University Hospital, Oslo, Norway e Bergen and Faculty of Odontology, University of Bergen, Oslo, Norway f Department of Surgical Oncology, The Norwegian Radium Hospital, Oslo, Norway g Department of Oral Pathology and Forensic Odontology, Haukeland University Hospital, Oslo, Norway |
| Abstract: | Fibrosarcoma is a rare tumour in children. The potential of malignancy has been questioned. We present three cases of fibrosarcoma in children. The follow-up periods range from 10 to 37 years. The first patient had pulmonary metastases at the time of diagnosis in 1958. The primary tumour in fossa ischio-rectalis was resected in 1960. Lung metastases were resected in 1960 and 1989. Radiotherapy was given in 1992. He is still alive with metastases 37 years after the first manifestation of disease. The second patient had a primary tumour and several local recurrences in the mandible. He is alive without evidence of disease 4 years after resection of pulmonary metastases and 21 years after resection of the primary tumour. The third patient has no signs of recurrence or metastasic spread 10 years after a wide excision of subcutanous tumours of the left upper arm. The cases demonstrate a special tumour-entity of low-grade malignancy, which show a good prognosis and a wide spectrum of biological behaviour. |
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