Transnodal lymphangiography and post-CT for protein-losing enteropathy in Noonan syndrome |
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Authors: | Tomohiro Matsumoto Takahiro Kudo Jun Endo Kazunobu Hashida Nao Tachibana Takatsugu Murakoshi |
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Institution: | 1. Department of Radiology, Tokai University Hachioji Hospital, Tokai University School of Medicine, Tokyo, Japan;2. Department of Gastroenterology, Tokyo Metropolitan Children’s Medical Center, Tokyo, Japan |
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Abstract: | Noonan syndrome, which is a multiple congenital disorder, may be associated with lymphatic abnormalities. Protein-losing enteropathy (PLE) developing in Noonan syndrome is rare. We performed transnodal lymphangiography by directly accessing bilateral inguinal nodes under ultrasound guidance in a 17-year-old female with PLE developing in Noonan syndrome to assess detailed anatomical findings regarding lymphatic vessels. There have been no reports on transnodal lymphangiography for Noonan syndrome. Post-lymphangiographic CT images revealed multiple lymphatic abnormalities and lipiodol extravasation into the duodenum and the proximal jejunum. Transnodal lymphangiography was easy and safe for PLE developing in Noonan syndrome, and post-lymphangiographic CT provided invaluable information. |
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Keywords: | Noonan syndrome transnodal lymphangiography CT protein-losing enteropathy |
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