Rare combination of hematuria due to drepanocytosis (sickle cell) in a white man

A case is presented of a white man with hematuria who was found to have sickle cell trait. When a cause for hematuria cannot be found, before making the diagnosis of “essential hematuria,” sickling of the erythrocytes and hemoglobin electrophoresis should be done, even in a white man. A distant relationship with a black person or persons of certain ethnic groups can be the cause of the disease presenting with this symptom. This case appears to be the second published in the literature and the first in Turkey.