法洛四联症肺动脉瓣缺如的外科治疗

目的 介绍法洛四联症肺动脉瓣缺如的外科治疗经验。方法 1985年1月-2000年9月，共治疗法洛四联症肺动脉瓣缺如13例，男10例，女3例。全组均在中低温体外循环下行根治手术；补片关闭室间隔缺损；解除处理右心室流出道梗阻；扩张的肺动脉部分切除整形，6例肺动脉区植入瓣叶。结果 术后死亡1例，死亡率7.7%，术后并发症包括；低心排出量3例，心包积液1例，经治疗均痊愈。结论 儿童型选择性根治处理原则同普通法洛四联症，婴幼儿型需立即手术根治并植入肺动脉瓣或带瓣管道解除右室流出道梗阻，瘤样扩张的肺动脉做部分切除和折叠整形。

Surgical treatment of tetralogy of Fallot with absent pulmonary valve

Objective To introduce the technique of surgical treatment of tetralogy of Fallot with absent pulmonary valve(TOF/APV) Methods From January 1985 to September 2000, 13 patients with TOF/APV underwent surgical correction at our hospital Results The post operative mortality was 7 7% (1/13) with no later death Surgical complications included low cardiac output in 3 cases, pericardial effusion in 1 case Eight patients suffered from pulmonary regurgitation (5 mild, 2 moderate, 1 severe with congestive heart failure) during the follow up of 1-3 years after surgery Conclusions We recommend that older children can be treated electively,while infants should be treated early The technique of partial resecting and plicating of dilated pulmonary artery and pulmonary valve implantation may improve outcome in patients with airway compression