多部位血管平滑肌脂肪瘤临床诊治分析

目的探讨人体多部位血管平滑肌脂肪瘤的临床病理特点和诊治状况，为建立合理的临床诊治规范提供部分依据。方法回顾性分析多部位血管平滑肌脂肪瘤156例的术前影像和病理诊断符合率及治疗方式和预后相关分析。结果156例血管平滑肌脂肪瘤中最多见的两个部位依次为肾脏 (77%, 120/156) 和肝脏 (14 %, 22/156)。81例(52%，81/156)肾脏及肝脏AML病例术前影像学和临床诊断为恶性或难以判定良恶性，其中74例按照恶性肿瘤根治原则采取根治性肾切除、肝脏介入治疗或肝叶切除。124例具有随诊结果，其中仅1例(0.8%, 1/124) 肾上皮样血管平滑肌脂肪瘤术后1年出现肝脏转移，其余病例平均随诊48月未见复发或转移。结论血管平滑肌脂肪瘤多累及肾脏和肝脏，绝大多数病例临床上显示为良性，未见复发或转移。因此，为避免良性肿瘤的过度治疗，术前穿刺和(或)术中冰冻病理诊断很有必要。

Clinical Analysis of Angiomyolipomas in Multiple Organs

Objective To investigate the clinical and pathological characterisitics and treatment conditions of angiomyolipomas occur in multiple parts of the body and establish a reasonable standard to provide some guide for clinical diagnosis and treatment.Methods Clinical-pathological features,concidence between preoperative image diagnosis and postoperative diagnosis,clinical treatments and follow-up results of 156 AMLs from 1981 to 2010 were retrospectively analyzed.Results The two common involved organs were kidn...