Pulmonary lymphangitic sarcomatosis and a review of the literature |
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Authors: | Gonlugur Tanseli Sapmaz Feride Katrancioglu Ozgur Gonlugur Ugur Elagoz Sahende |
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Affiliation: | (1) Department of Chest Diseases, Canakkale State Hospital, 17100 Canakkale, Turkey;(2) Department of Thoracic Surgery, Sivas State Hospital, 58040 Sivas, Turkey;(3) Department of Chest Diseases, Onsekiz Mart Universitesi Tip Fakultesi, Onsekiz Mart University Medical School, Gogus Hastaliklari Anabilim Dali, 17100 Canakkale, Turkey;(4) Department of Pathology, Cumhuriyet University Medical School, 58140 Sivas, Turkey |
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Abstract: | Intrapulmonary spread of a sarcoma via lymphatics is a rare cause of death in a young adult. A 31-year old man was admitted to our hospital complaining of dyspnea and malaise of 2 months’ duration. A chest radiography revealed bilateral hilar enlargement, and reticulonodular infiltrations. Thoracic CT-scans demonstrated mediastinal lymphadenopathy, thickening of interlobular septa, polygonal lines, and thickening of bronchovascular bundles. The diagnosis was made by open-lung biopsy. The patient died within 3 months after diagnosis. Pulmonary lymphangitic sarcomatosis is a rare but important manifestation of an angiosarcoma. Optimal treatment of these patients is not well defined, but a trial of chemotherapy may be warranted. |
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Keywords: | Computed tomography Lung neoplasms Lymphangitis Lymphatic metastasis |
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