Antisynthetase syndrome without muscle involvement |
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Authors: | Júdez Navarro Enrique Martínez Carretero Myriam Martínez Jiménez Gonzalo Fidel |
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Affiliation: | 1. Servicio de Reumatología. Hospital Virgen del Perpetuo Socorro. Albacete. España;2. Medicina Familiar y Comunitaria. Hospital General Universitario de Albacete. Albacete. España;1. Department of Microbiology and Institute for Immunology, Perelman School of Medicine, University of Pennsylvania, 331 Biomedical Research Building II/III, 421 Curie Boulevard, Philadelphia, PA 19104, USA;2. Medical Research, Philadelphia Corporal Michael J. Crescenz VA Medical Center (CMC VAMC), A424, University and Woodland Avenue, Philadelphia, PA 19104, USA;3. Division of Gastroenterology, Department of Medicine, Perelman School of Medicine, University of Pennsylvania, 421 Curie Boulevard, Philadelphia, PA 19104, USA;1. Hospital María Ferrer, Buenos Aires, Argentina;2. Instituto Nacional del Tórax, Santiago, Chile;3. Instituto Nacional de Enfermedades Respiratorias Ismael Cosio Villegas, Ciudad de México, Mexico;4. Hospital Juan A. Fernández, Buenos Aires, Argentina;1. Service de médecine interne, pôle hospitalo-universitaire 3, centre de compétences maladies systémiques et auto-immunes rares, hôpital Hôtel-Dieu, place Alexis-Ricordeau, 44093 Nantes cedex 1, France;2. Clinique cardiologique et des maladies vasculaires, pôle hospitalo-universitaire 2, hôpital Nord Laënnec, boulevard Jacques-Monod, 44093 Nantes cedex 1, France;3. Service de pneumologie, pôle hospitalo-universitaire 2, hôpital Nord Laënnec, boulevard Jacques-Monod, 44093 Nantes cedex 1, France;4. Inserm UMR1087, CNRS UMR6291, unité de recherche de l’institut du thorax, équipe 2 « Signalisation et hypertension artérielle », IRS université de Nantes, 8, quai Moncousu, BP70721, 44007 Nantes cedex 1, France |
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Abstract: | Antisynthetase syndrome is a well defined syndrome characterized by the presence of interstitial lung disease in association with arthritis, miositis, mechanic's hands and Ruynaud's phenomenon in the presence of antisynthetase antibodies, especially Ac anti-Jo1. We described the case of a 68-year-old man with this syndrome in the absence of inflammatory muscle disease. |
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