An infrequent presentation of SAPHO syndrome |
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Authors: | Centeno Jiménez Miriam Díaz-Delgado Peñas Rafael Calvo Rey Cristina Collado Paz |
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Affiliation: | 1. Departamento de Sistemática e Ecologia, CCEN, Universidade Federal da Paraíba, Laboratório de Termitologia, 58051-900 João Pessoa, PB, Brazil;2. Universidade Federal do Piauí, Campus Professora Cinobelina Elvas, Bom Jesus, PI 64900-000, Brazil;3. Programa de Pós-Graduação em Ciências Farmacêuticas, Universidade Estadual da Paraíba, Campina Grande, Paraíba 58.429-500, Brazil;4. Laboratório de Desenvolvimento e Ensaios de Medicamentos, Centro de Ciências Biológicas e da Saúde, Universidade Estadual da Paraíba, Campina Grande, Paraíba 58.429-500, Brazil;5. Laboratório de Microbiologia e Biologia Molecular, Universidade Regional do Cariri, Crato, CE 63105-000, Brazil;6. Departamento de Biologia, Universidade Estadual da Paraíba, Laboratório de Termitologia, 58051-900 João Pessoa, PB, Brazil;1. Cotton University, Guwahati, India;2. Centre for Atmospheric and Oceanic Sciences & Divecha Centre for Climate Change, Indian Institute of Science, Bangalore, India;3. Indian Institute of Tropical Meteorology, Pune, India |
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Abstract: | We describe a case of SAPHO (synovitis, acne, pustulosis, hyperostosis and osteitis) with an unusual presentation in a 14 year-old girl with low grade fever which lasts 8 months, left low back pain and elevated erythrocyte sedimentation rates and protein C-reactive with chronic anaemia. A radiograhy of the lower limbs showed a lytic image with osteitis and hyperostose in the right fibula, as a casual finding. This information, in addition to the acne, pustulosis, sternoclavicular arthritis and the studies got from the magnetic resonance image (MR) of spine, pointed out the diagnosis of SAPHO. |
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