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Right Ventricular Involvement of an Aggressive Malignant Peripheral Nerve Sheath Tumor |
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| Authors: | Saikrishna Patibandla Miklos Auber Stell Patadji Yasmin Hamirani |
| Institution: | 1.Department of Cardiology, West Virginia University Heart and Vascular Institute, Morgantown, WV, USA; 2.Department of Hematology & Oncology, West Virginia University, Morgantown, WV, USA; 3.Department of Pathology, West Virginia University, Morgantown, WV, USA |
| Abstract: | We present a case of a 58-year-old woman who had a painful right thigh mass for a few months. A transthoracic echocardiogram revealed no evidence of an intracardiac mass. She had a whole-body positron emission tomography/computed tomography scan two months later that revealed masses in her right lower extremity and a mass in her right ventricle that had not been initially reported. She had been initially diagnosed with an undifferentiated pleomorphic sarcoma, but this diagnosis was changed to a malignant peripheral nerve sheath tumor with repeat pathology. She was subsequently hospitalized. An echocardiogram showed a mass covering 80% of her right ventricle (RV). Serial cardiac magnetic resonance imaging revealed a 9.4 × 5.6 cm RV mass with vascular and avascular portions and inflow and outflow tract obstruction. Computed tomography showed no other metastases. Due to a delay in diagnosis and a decline in left ventricular ejection fraction, the patient could not undergo palliative chemotherapy or radiotherapy |
| Keywords: | Malignant peripheral nerve sheath tumor cardiac magnetic resonance imaging transthoracic echocardiography peripheral magnetic resonance imaging cardiac metastasis |