Enfermedad pulmonar intersticial difusa por metaplasia peribronquiolar |
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Authors: | Esteban Cano-Jiménez María Molina-Molina José Ramírez Marcelo Sánchez Joan Lluis Aliaga Antoni Xaubet |
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Affiliation: | 1. Servicio de Neumología, Hospital Clínic, Universitat de Barcelona, Barcelona, España;2. Servicio de Anatomía Patológica, Hospital Clínic, Universitat de Barcelona, Barcelona, España;3. Servicio de Radiodiagnóstico, Hospital Clínic, Universitat de Barcelona, Barcelona, España;4. Servicio de Neumología, Hospital de Barcelona-SCIAS, Barcelona, España |
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Abstract: | Peribronchiolar metaplasia is a histologic lesion characterized by fibrosis and bronchiolar epithelial proliferation, affecting peribronchiolar alveolar septa and terminal bronchioles. It has been considered a nonspecific tissue reaction secondary to the action of external factors, such as tobacco smoke and microbes, and is a common histologic finding in several diffuse interstitial lung diseases. Several such cases with clinical, radiologic, and lung function manifestations characteristic of idiopathic interstitial pneumonia have been described recently, all having peribronchiolar metaplasia as the only histologic abnormality. We report 2 cases of interstitial lung disease in which peribronchiolar metaplasia was the only finding of pathology. |
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