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罕见乏脂纵隔血管平滑肌脂肪瘤1例并文献复习
引用本文:张毅,潘铁成,魏翔. 罕见乏脂纵隔血管平滑肌脂肪瘤1例并文献复习[J]. 临床肺科杂志, 2010, 15(1): 7-9
作者姓名:张毅  潘铁成  魏翔
作者单位:华中科技大学同济医学院附属同济医院心胸外科,武汉,430030
摘    要:目的探讨乏脂纵隔血管平滑肌脂肪瘤的临床、病理特征和鉴别诊断。方法1例纵隔乏脂血管平滑肌脂肪瘤,同时结合国内外文献复习。结果1例46岁术前诊断为纵隔肿瘤,全麻下行纵隔肿瘤切除术。术后诊断为纵隔乏脂血管平滑肌脂肪瘤,组织学特征与其他部位血管平滑肌脂肪瘤相似,免疫组化表达HMB45、S-100、Des。结论本例罕见,诊断依靠临床、病理学特征及免疫组化三方面结合。乏脂纵隔血管平滑肌脂肪瘤必须经过全面思维和细致检查,以求正确诊断,为决策正确治疗提供科学依据。

关 键 词:纵隔  血管平滑肌脂肪瘤  诊断  治疗

One-case-study of rare mediastinal angiomyolipoma of absent fat and literature review
ZHANG Yi,PAN Tie-cheng,WEI Xiang. One-case-study of rare mediastinal angiomyolipoma of absent fat and literature review[J]. Journal of Clinical Pulmonary Medicine, 2010, 15(1): 7-9
Authors:ZHANG Yi  PAN Tie-cheng  WEI Xiang
Affiliation:( Department of Cardiothoraeic Surgery, Tongji Hospital ,Huazhong University of Science and Technology, Wuhan 430030, China)
Abstract:Objective To discuss the clinical and pathological characteristics of mediastinal angiomyolipom of absent fat and its differential diagnosis.Methods One case of mediastinal angiomyolipoma of absent fat was observed with HE and immunohistochemical stains and the literature review was conducted.Results Although the true diagnosis was missing preoperatively,complete excision of the tumor was achieved via a right 4 th inter-rib posterior-lateral incision.The resected specimen was an encapsulated mass measuring ...
Keywords:mediastinum  angiomyolipoma  diagnosis  treatment  
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