大前庭导水管综合征临床分析

目的探讨大前庭导水管综合征(LVAS)的发病、临床表现及防治措施。方法对25例经高分辨率CT证实为双侧LVAS患者的诊疗过程进行回顾性分析。结果25例患者全部有严重的听力损失,15例听力有波动性,3例有头颅外伤史。在CT图像上,23例双侧和1例单侧有前庭导水管扩大。MRI图像上,5例双侧、1例单侧内淋巴管和内淋巴囊均有扩大.急性发作期患儿经过营养神经、扩张血管、糖皮质激素治疗,听力提高,达到或接近发作前水平。结论LVAS是一种独立的疾病,极易误诊,对临床上有波动性进行性听力下降、轻微的头颅外伤引起严重的听力下降的患者或声发射测定结果波动较大的感音神经性聋患者,应常规进行颞骨高分辨率CT扫描,以明确诊断,对已经证实的患者应积极进行干预治疗,尽可能地保存患者的残余听力。

The Clinical Analysis of Large Vestibular Aqueduct Syndrome Patients

Objective To explore the clinical manifestation,prevention and treatment of large vestbular aqueduct syndrome (LVAS). Methods The clinical process of diagnosis and treatment of 25 patients with LVAS confi rmed by high resolution CT were retrospectively analyzed. Results All the cases had grave sensorineural hearing loss,of whom,15 were diagnosed with fluctuating hearing. Most of the cases examined were found with pathological changes in vestibular aqueduct enlargement after high resolution CT scan and MRI i...