肺并发肝上皮样血管内皮瘤影像表现(附3例报告并文献复习)

目的:探讨肺并肝上皮样血管内皮细胞瘤的影像学表现,提高对其认识。方法:回顾性分析3例肺并发肝上皮样血管样内皮细胞瘤,结合文献对其临床表现、影像学诊断、及预后进行分析。结果:该病病因不清,临床可无症状或症状较少且轻微,可表现为咳嗽、咯痰,影像学CT检查主要表现为两肺多发性小结节影,肝内病灶多可见钙化,病理学检查主要特征是单细胞原始管腔结构,免疫组织化学提示内皮细胞源性。患者预后介于良、恶性肿瘤之间。结论:肺并肝上皮样血管内皮瘤罕见,极易误诊,应予重视。

Pulmonary complicated with hepatic epithelioid hemangioendothelioma: 3 cases report and review of the literature

Objective：To explore the characters of pulmonary epithelioid hemangioendothelioma and improve the diagnosis.Methods：With 3 cases reported and review of the related literatures,the etiology,clinical manifestations,imaging diagnosis,clinical diagnosis,prognosis of pulmonary epithelioid hemangioendothelioma were described.Results：The etiology of this rare disease remains unknown,Symptoms are scanty and usually mild;chest radiograph or computed tomography usually reveals multiple bilateral pulmonary nodules.Primitive lumen formed by a single cell is the pathologic feature,immunohistochemical stains show that the malignant cell of the endothelial type.Conclusion：Pulmonary epithelioid hemangioendothelioma is rare and often misdiagnosed as other pulmonary diseases.