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多系统萎缩患者的临床表现、MRI、肛门括约肌肌电图分析
引用本文:程卫国,李红勤,张剑平,汤群峰.多系统萎缩患者的临床表现、MRI、肛门括约肌肌电图分析[J].中风与神经疾病杂志,2011,28(7).
作者姓名:程卫国  李红勤  张剑平  汤群峰
作者单位:1. 南京医科大学附属无锡人民医院神经内科,江苏,无锡,214009
2. 南京医科大学附属无锡人民医院肌电图室,江苏,无锡,214009
3. 南京医科大学附属无锡人民医院放射科,江苏,无锡,214009
摘    要:目的分析多系统萎缩患者(MSA)临床表现、头部MRI、肛门括约肌肌电图改变特点,探讨它们在MSA诊断的价值。方法按Gilman诊断标准,回顾性分析46例MSA患者的临床资料、头部MRI及肛门括约肌肌电图检查结果。结果符合很可能MSA39例,可能MSA7例,其中MSA-A型24例,主要临床表现为自主神经功能障碍;MSA-C型16例,主要表现为小脑性共济失调;MSA-P型6例,主要表现为锥体外系症状。MRI显示部分MSA-A患者出现大脑皮质萎缩,小脑改变较轻;MSA-C型主要表现为延髓、脑桥、小脑萎缩;MSA-P主要病变在壳核和苍白球,而小脑、脑桥、延髓病变早期可以不明显。部分患者出现脑桥十字征和壳核裂隙征。36例患者做肛门括约肌肌电图检查,全部出现神经源性损害。结论 MSA早期诊断难度大,结合临床表现、头部MRI检查及肛门括约肌肌电图检查,可提高MSA的诊断准确率。

关 键 词:多系统萎缩  MRI  肌电描记术  

Clinical expressions,magnetic resonance imaging and external anal sphincter electromyography analysis on multiple system atrophy
CHENG Wei-guo,LI Hong-qin,ZHANG Jian-ping,et al..Clinical expressions,magnetic resonance imaging and external anal sphincter electromyography analysis on multiple system atrophy[J].Journal of Apoplexy and Nervous Diseases,2011,28(7).
Authors:CHENG Wei-guo  LI Hong-qin  ZHANG Jian-ping  
Institution:CHENG Wei-guo,LI Hong-qin,ZHANG Jian-ping,et al.(Department of Neurology,Wuxi People Hospital Affiliated to Nanjing Medical University,Wuxi 214009,China)
Abstract:Objective To evaluate the clinical expressions,magnetic resonance imaging and external anal sphincter electromyography features of 46 patients with multiple system atrophy(MSA)for correct diagnosis.Methods The clinical datas of 46 cases diagnosed as MSA based on Gilman diagnostic criteria were recuited in a retrospective studied.Clinical expressions,magnetic resonance imaging and external anal sphincter electromyography(EAS-EMG)data were retrospectively analyzed.Results In 46 cases,39 cases were probably di...
Keywords:Multiple system atrophy  Magnetic resonance imaging  Electromyography  
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