Effective treatment of hereditary angioedema with fresh frozen plasma in an emergency department |
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Authors: | Pekdemir Murat Ersel Murat Aksay Ersin Yanturali Sedat Akturk Aysun Kiyan Selahattin |
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Affiliation: | Department of Emergency Medicine, Kocaeli University Hospital, Izmit, Turkey. |
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Abstract: | Hereditary angioedema (HAE) is a rarely seen disorder of C1 inhibitor (C1-INH) deficiency usually manifested by non-pruritic swelling of the skin. Acute exacerbations are not sensitive to conventional medications, and C1-esterase inhibitor concentrates are recommended as the first-line therapy. However, fresh frozen plasma is the main treatment alternative in many centers due to the lack of C1-esterase inhibitor concentrates. In this report, we present 3 patients with acute exacerbations of hereditary angioedema who were effectively and safely treated with fresh frozen plasma. |
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Keywords: | hereditary angioedema fresh frozen plasma emergency department |
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