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Acute intrahepatic portal vein thrombosis complicating cholangitis in biliary atresia
Authors:C. Cuffari  E. Seidman  J. DuBois  P. Brochu  F. Alvarez
Affiliation:Service de Gastroentérologie-Nutrition, H?pital Sainte-Justine, 3175, C?te Ste-Catherine, Montréal (Québec), H3T 1C5 Canada, Tel.: (514) 345–4626, Fax: (514) 345–4999, CA
Division of Radiology, H?pital Sainte-Justine, Montréal, Canada, CA
Division of Pathology, H?pital Sainte-Justine, Montréal, Canada, CA
Abstract:A 2-year-old boy with a Kasai portoenterostomy had systemic features suggestive of cholangitis and acute portal vein obstruction. The rapid rise in portal pressure caused a transient, severe decompensation of hepatic function. A superior mesenteric arterial angiogram confirmed the presence of diffuse intrahepatic portal vein thrombosis. Conclusion This case provides clinical and radiological evidence supporting an association between ascending cholangitis and acute intrahepatic portal vein thrombosis. Received: 7 May 1996 / Accepted: 3 September 1996
Keywords:Biliary atresia  Cholangitis  Intrahepatic portal vein thrombosis
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