Desmoplastic fibroma of bone: a report of 18 cases |
| |
Authors: | W K Taconis H E Schütte R O van der Heul |
| |
Institution: | (1) Department of Diagnostic Radiology, Onze Lieve Vrouwe Gasthuis, 1e Oosterparkstraat 179, NL-1091 HA Amsterdam, The Netherlands;(2) Department of Diagnostic Radiology, University Hospital, Rotterdam, The Netherlands;(3) Department of Pathology, Academic Medical Center, Amsterdam, The Netherlands |
| |
Abstract: | Desmoplastic fibroma is a rare benign primary bone tumor, histologically identical to the extra-abdominal desmoid tumor of
soft tissues. The incidence in major series of bone tumors is 0.1%–0.3%. In the present study 18 cases from the files of the
Netherlands Committee on Bone Tumors are reported, with an emphasis on the radiographic features. Eight female and ten male
subjects were affected, with a fairly even age distribution from the second to the seventh decade of life. The most frequent
sites of involvement were the femur and the pelvis. Radiographically the lesions nearly always demonstrated benign features
with respect to pattern of destruction, margins, and reactive bone formation; however, soft tissue extension was sometimes
present. Although desmoplastic fibroma usually presents with pain or swelling, in 5 of the 18 cases the existence of the lesion
was an accidental finding, and in 2 cases the patient had long-standing, vague complaints of pain. Though overall benign radiographic
features may support the final diagnosis, the main and often troublesome histological differential diagnosis is of a low-grade
fibrosoma. En bloc resection is the treatment of choice in view of the high incidence of recurrence after curettage. |
| |
Keywords: | Neoplasms Bone tumors Desmoplastic fibroma |
本文献已被 SpringerLink 等数据库收录! |
|