肺郎格汉斯细胞组织细胞增生症的CT表现及文献复习

目的 探讨肺郎格汉斯细胞组织细胞增生症（PLCH）的CT表现，提高对该病的认识。资料与方法 回顾性分析2例病理证实的PLCH患者的临床和CT资料。2例患者行多次胸部CT检查，其中1例为戒烟3年后复查，另1例因反复气胸复查。结果 1例早期PLCH的CT表现为双肺以中上肺野为主广泛分布的小片状、结节状、小环状病灶，戒烟后病灶吸收：1例晚期PLCH的CT表现为双肺以中肺野为主广泛分布的大小不等的圆形、类圆形低密度透光区，部分呈囊状和蜂窝状改变．并合并反复气胸。结论 PLCH的CT表现有一定特征性，结合临床可提高对此病的诊断。

CT Findings of Pulmonary Langerhans Cell Histiocytosis

Objective To study the CT findings of pulmonary Langerhans cell histiocytosis and to make a further understanding of the disease. Materials and Methods Clinic and CT data of 2 cases with pulmonary Langerhans cell histiocytosis were analyzed retrospectively, CT scan was performed many times in 2 cases, 1 case was reviewed after having stopped smoking for 3 years and another because of repeated pneumothorax. Results CT manifestations of 1 case with earlier stage of PLCH were multiple, micropatchy, nodular, microannular lesion, which were distributed more throughout both upper and middle lung fields and disappeared after he had stopped smoking. CT manifestations of another case with advanced stage of PLCH were multiple, different sized eystoid transparent areas, with some cysts being coalesced together to form honeycomb, which were distributed throughout more in both middle lung fields and caused repeated pneumothorax. Conclusion PLCH has special changes in CT findings, combing CT findings with clinical data for PLCH can make a correct diagnosis.