Spectrum of cardiovascular lesions in mucocutaneous lymph node syndrome: Analysis of eight cases |
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Authors: | Junichiro Fukushige Michael R Nihill Dan G McNamara |
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Institution: | From The Lillie Frank Abercrombie Section of Cardiology, Department of Pediatrics, Baylor College of Medicine, and the Texas Children''s Hospital, Houston, Texas, USA |
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Abstract: | Eight cases of mucocutaneous lymph node syndrome with cardiovascular complications are described. The clinical presentation in all but one patient conformed to the previously described features of this syndrome. Five patients had cardiac enlargement, six had electrocardiographic abnormalities and three had a murmur of mitral insufficiency. Each of the four patients who died had aneurysms of the coronary arteries, usually associated with organizing thrombi. In addition to involvement of the coronary arteries, the renal, mesenteric, vertebral, splenic, hepatic and iliac arteries were affected in individual cases. One patient required triple aortocoronary bypass surgery and one patient underwent excision of a brachial arterial aneurysm. Further long-term follow-up studies of the patients who have survived the acute stage of the syndrome are indicated to establish the spectrum of late complications and sequelae. |
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Keywords: | Address for reprints: Michael R Nihill MD Section of Pediatric Cardiology Texas Children's Hospital 6621 Fannin Houston Texas 77030 |
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