肾上皮样血管平滑肌脂肪瘤临床诊治分析

目的：探讨肾上皮样血管平滑肌脂肪瘤（REA）的临床特点和诊治方法.方法：回顾性分析2007年3月-2013年1月我院收治的13例REA的临床资料,分析其临床、病理、治疗和预后的特点.结果：术前诊断为肾血管平滑肌脂肪瘤（AML）7例.所有患者均行手术治疗,术后免疫组化分析支持REA诊断.9例获得随访,随访时间4-74个月,平均31个月.无瘤存活6例.结论：REA是一种少见的具有恶性潜能的肿瘤,诊断需要与肾细胞癌（RCC）相鉴别.免疫组化能够确诊,术后需要密切随访.

Diagnosis and therapy of renal epithelioid angiomyolipoma

Objective：To investigate the clinical characteristics,diagnosis and treatment of renal epithelioid angio- myolipoma（REA）. Methods：A retrospective study was accomplished on 13 patients of REA ll＇om March 2007 to Jan- uary 2013. The clinical findings,pathologic features,treatment and prognostic characteristics were evaluated. Results： Seven cases were diagnosed as renal angiomyolipoma（AML） preoperatively. All the cases were treated by surgery, Im- munohistochemical analysis supported REA after surgery. 9 cases were followed for 31 months （ranging 4 - 74 months）. 6 patients survived with tumor- free. Conclusion：REA is a rarely potentially malignant neoplasm, it needs to identify with renal cell carcinoma before diagnosis, Immunohistochemical staining can be used for diagnosis. Follow- ing up closely is needed.