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Protein Substitute Requirements of Patients with Phenylketonuria on BH4 Treatment: A Systematic Review and Meta-Analysis |
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| Authors: | Fatma Ilgaz Cyril Marsaux Alex Pinto Rani Singh Carmen Rohde Erdem Karabulut Hülya Gkmen- zel Mirjam Kuhn Anita MacDonald |
| Abstract: | |
| Keywords: | phenylalanine hydroxylase deficiency hyperphenylalaninemia PKU protein substitute medical formula amino acid mixture tetrahydrobiopterin sapropterin BH4 |