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An unusual case of primary systemic amyloidosis
Authors:L. Ambrosone  L. Mansi  T. Salvatore  F. Marino   P. Orabona  A. Rambaldi  P.F. Rambaldi  M. Rambaldi
Affiliation:Istituto di Clinica Medica-Reumatologia, Seconda Universitàdi Napoli, Naples, Italy;Istiluto di Scienze Radiologiche-Medicina Nucleare, Seconda Universitàdi Napoli, Naples, Italy;Istituto di Medicina Interna e Malattie Metaboliche, Seconda Universitàdi Napoli, Naples, Italy;lstituto di Clinica Dermosifilopatica, Seconda Universitàdi Napoli, Naples, Italy;Istituto di Anatomia Patologica, UniversitàFederico II di Napoli, Naples, Italy
Abstract:Here we report an unusual case of primary systemic amyloidosis. The cutaneous lesions were polymorphic and included involvement of both external auditory canals. The visceral involvement was covert. Mapping of amyloid deposits was performed using scintigraphy with technetium-99m (V) dimercaptosuccinic acid ([99mTc (V)] DMSA). Therapy with melpha-lan, prednisone and colchicine resulted in considerable improvement.
Keywords:Amyloidosis    External auditory canals    Scintigraphy with technetium-99m (V) dimercaptosuccinic acid ([99mTc (V)] DMSA)    Therapy
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