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Kasabach-Merritt综合征研究进展
引用本文:夏红萍,蔡康,朱建幸.Kasabach-Merritt综合征研究进展[J].国际儿科学杂志,2010,37(1).
作者姓名:夏红萍  蔡康  朱建幸
作者单位:上海交通大学医学院附属新华医院儿内科,200092
摘    要:Kasabach-Merritt综合征是以巨大血管肿瘤伴发血小板减少和全身出血倾向为特征的一种综合征,其病理生理基础是血小板减少和弥漫性血管内凝血(DIC),与巨大血管肿瘤密切相关.治疗方案主要包括纠正DIC和血小板减少,根据具体情况选择外科治疗(手术切除、栓塞等)或内科药物治疗(糖皮质激素、α-干扰素、免疫抑制剂等)去除血管肿瘤.

关 键 词:Kasabach-Merritt综合征  血小板减少  血管肿瘤

Progress in Kasabach-Merritt syndrome
XIA Hong-ping,CAI Kang,ZHU Jian-xing.Progress in Kasabach-Merritt syndrome[J].International Journal of Pediatrics,2010,37(1).
Authors:XIA Hong-ping  CAI Kang  ZHU Jian-xing
Abstract:Kasabach-Merritt syndrome(KMS) is a massive haemangioma with thrombocytopenia and consumptive coagulopathy. The histopathology of KMS is thrombocytopenia and disseminated intravascular coagulation associated with massive haemangioma.A standard treatment regimen for KMS has not been established. Therapy includes surgery, embolism and medicine(steroids,α-interferon , immunosuppressant , etc).
Keywords:Kasabach-Memtt syndrome  Haemangioma  Thrombocytopenia
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