超声心动图诊断永存左位上腔静脉引流入左心房的价值

目的探讨超声心动图对永存左位上腔静脉引流入左房的诊断价值。方法对我院行超声心动图检查并经手术证实的13例永存左位上腔静脉（PLSVC）引流入左房病例进行了回顾性分析，总结不同引流途径的超声表现并与手术结果相对照。结果PLSVC直接开口于左房8例，PLSVC接冠状静脉窦（CS）合并CS终末段缺如者3例，PLSVC接CS合并CS中间段缺损者1例，PLSVC接CS合并CS中间、终末段均缺损者1例。7例行右心超声造影。超声正确诊断6例，误诊或漏诊7例。其中8例Raghib综合征漏诊4例，3例PLSVC接CS合并CS终末段缺如仅诊断为PLSVC2例，误诊为Raghib综合征1例。结论超声心动图结合右心超声造影可作为PLSVC引流入左房患者术前诊断的首选和筛选方法。

Echocardiographic diagnosis of persistent left superior vena cava draining into the left atrium

Objective To explore the value of transthoracic echocardiography in diagnosing persistent left superior vena cava(PLSVC)draining into left atrium (LA). Methods The echocardiographic characteristics of 13 patients with PLSVC draining into LA via different pathways were analyzed retrospectively and compared with surgical results.Results Among 13 patients with PLSVC,8 PLSVCs draining into LA directly,3 PLSVCs draining into coronary sinus (CS) with partially unroofed terminal-portion of CS,1 PLSVC draining into LA with unroofed mid-portion of CS,and 1 PLSVC draining into LA with both unroofed terminal and mid-portion of CS.Among them,7 patients underwent contrast echocardiography.Echocardiography diagnosed 6 cases correctly.Other 7 cases were misdiagnosed or remained undiagnosed.Among them 4 patients with Raghib syndrome were missed diagnosis,1 with PLSVC draining into CS with partially unroofed terminal-portion of CS was misdiagnosed as Raghib syndrome,and in the remaining 2 cases only PLSVCs were found.Conclusions Transthoracic echocardiography combined with contrast echocardiography may be the preferred screening method in diagnosing PLSVC draining into LA.