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A child with CARD14-associated papulosquamous eruption (CAPE) successfully treated with ustekinumab
Authors:Miguel Nogueira MD  Joel Reis MD  Maria Abreu MD  André Coelho MD  Cláudia F. Reis MD  Susana Machado MD
Affiliation:1. Dermatology Department, Centro Hospitalar Universitário de Santo António, Porto, Portugal;2. Medical Genetics Center Dr. Jacinto Magalhães, Centro Hospitalar Universitário de Santo António, Porto, Portugal;3. Pathology Department, Centro Hospitalar Universitário de Santo António, Porto, Portugal
Abstract:CARD14-associated papulosquamous eruption (CAPE) is a rare inflammatory skin eruption that can have features of psoriasis, pityriasis rubra pilaris, and erythroderma. This skin condition is known for its resistance to topical or conventional systemic therapies. Successful treatment of CAPE with anti-IL-12/IL-23 and IL-17 inhibitors has been reported. We present a case of a 2-year-old girl with CAPE who was successfully treated with ustekinumab.
Keywords:erythroderma  pediatric  ustekinumab
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