胼胝体发育不全的MRI诊断

目的探讨胼胝体发育不全的MRI特征性表现.材料和方法回顾性分析14例胼胝体发育不全的MRI表现,并从组织胚胎学、形态学及病理的角度加以分析解释.结果本组胼胝体发育不全分为3型完全缺如2例,其中1例可见双侧Probst束;部分缺如10例;胼胝体完整性存在的但呈整体性或部分性变小2例.7例伴有其他先天性脑部畸形,包括脂肪瘤、灰质异位、脑裂畸形、多小脑回以及透明隔缺如等.结论MRI是诊断胼胝体发育不全及其合并的其他脑部畸形最理想的诊断手段.

MR Diagnosis of Dysplasia of Corpus Callosum

Purpose: To investigate the MRI features of dysplasia of corpus callosum. Materials and Methods: MRI findings of 14 cases with dysplasia of corpus callosum were retrospectively analyzed and discussed based on the embryological, morphological and pathological changes. Results: Three types of corpus callosal dysgenesis were recognized: total defect (n=2, bilateral Probst's bundles were identified in one case). partial defect (n=10); intact corpus callosum with total or partial hypoplasia (n=2). The associated congenital anomalies were also observed in 7 of 14 cases, including lipoma, gray matter heterotopia, schizencephaly, polymicrogyria, and deficient septum pellucidum. Conclusion: MR imaging is an ideal method of choice for diagnosing the dysplasia of corpus callosum and other associated congenital cerebral anomalies.