先天性肾发育不良并输尿管异位开口诊治分析

目的 探讨小儿先天性单肾发育不良合并输尿管异位开口的病因、诊断与治疗。方法 总结分析自1984年以来15例经手术确诊为先天性单肾发育不良合并输尿管异位开口的临床资料。结果 15例患者均为女性，其中2例为亲姐妹．11例输尿管异位开口于阴道，4例开口于前庭。静脉尿路造影（IVU）患肾均不显影，对侧肾代偿性增大，常规B超均未能明确探及患肾。B超检查10例，6例发现患肾；彩色多普勒超声（CDI）检查8例，6例发现患肾；CT扫描7例，3例提示腹膜后有发育不良肾影。所有患者均经手术治疗而愈。结论 先天性单肾发育不良合并输尿管异位开口可能具有遗传倾向，B超和CDI有助于提高术前诊断阳性率，手术切除发育不良肾脏及输尿管疗效确切。

The diagnosis and treatment of renal dysplasis with single ectopic ureter

Objective To study the diagnosis cause and treatment of renal dysplasia with single eetopic ureter. Methods Since 1984,clinical records of 15 patients were analyzed. Results All 15 patients were female,2 patients were sister. Vaginal ectopic ureters were observed on 11 eases and vestibular cetopie ureters on 4. IVU showed absence of kidney on one side and compensatory hypertrophy on the opposite side. Regular US failed to demonstrate the dysplastic kidney. Dysplastic kidneys were correctly located and diagnosed by dinretie US in 6/10 eases and by CDI in 6 out of 8 eases. All 15 patients had got satisfactory results. Conclusions Congenital renal dysplasia with single ectopie ureter maybe is a inherited disease. Dinretic US and CDI are the recommended method of investigations. Ureteronephrcetomy of dysplastic kidney should be the treatment of choice.