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先天性肝内胆管囊状扩张症
引用本文:晏仲舒,张时绥,胡全美,许雪峨. 先天性肝内胆管囊状扩张症[J]. 中南大学学报(医学版), 1984, 0(1)
作者姓名:晏仲舒  张时绥  胡全美  许雪峨
作者单位:湖南医学院第一附属医院外科(晏仲舒,张时绥),湖南医学院第一附属医院儿科(胡全美),湖南医学院第一附属医院儿科(许雪峨)
摘    要:先天性肝内胆管囊状扩张少见,由经皮肝穿刺胆管造影(以下简称PTC)术前确诊者国内尚未见报道,现报告二例。 例一 男,2岁半,住院号258914,因发热月余,腹泻十余日,发现肝脾肿大于82年8月31日入院。患儿自半岁起腹部逐渐增大,食欲减退,间歇发热,无腹痛呕吐及皮肤发黄。足月第5胎,父曾患胆石症。体查:体温38°6C,脉搏120次,发育尚好,营养差,慢性病容,无黄疸,心肺无异常。腹膨隆,未见静脉曲张。肝在右肋缘下6厘米,剑突下5厘米。脾在右肋下缘5厘米,无腹水征。血清茶丙转氨酶、麝香草酚浊度

关 键 词:囊状扩张  胆管  先天性

CONGENITAL CYSTIC DILATION OF THE INTRAHEPATIC BILIARY DUCTS
Yan Zhongshu Zhang Shisui. CONGENITAL CYSTIC DILATION OF THE INTRAHEPATIC BILIARY DUCTS[J]. Journal of Central South University. Medical sciences, 1984, 0(1)
Authors:Yan Zhongshu Zhang Shisui
Affiliation:Yan Zhongshu Zhang ShisuiDepartment of Surgery,The First Affiliated Hospital Hunan Medical CollegeHu Quanmei Xu Xue-eDepartment of Pediatrics,The First Affiliated Hospital Hunan Medical College
Abstract:Two cases of congenital dilatation of intrahepatic biliary ducts(Caroli's disease) are reported, both were boys 2+ and 4+ years of age. The diagnosis was established by echography and percutaneous transhepatic cholangiography. Case 1 was operated on and a left hepatojejunostomy was constructed. Case 2 had apparent hepatic fibrosis associated with portal hypertesion, operation was refused.
Keywords:Cystic dilatation Biliary duct Congenital
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