Congenital absence of portal vein in a girl with biliary atresia treated with liver transplant |
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Authors: | Taoube K A Alonso Calderón J L Yandza T St Vil D Blanchard H |
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Affiliation: | Hopital Sainte-Justine, Montréal, Quebec, Canadá. |
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Abstract: | The congenital absence of the portal vein is a rare malformation, which has been generally discovered in association with another anomalies like a cardiac, gastrointestinal or genitourinary defects. With portal hypertension and hepatic cirrhosis, this anomaly is similar to spontaneous porto-systemic derivation, and for that not collateral venous drainage is present. In these patients, total interruption of mesentaric venous drainage during procurement of liver transplant produce a very important bowel and mesenteric edema, which can promote an injert fatal evolution. The authors present the first paediatric liver transplant, in a patient with portal venous agenesia, with de piggy-back technique was done and this complication was obviated, and a review of the literature about this issue is done. |
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