Giant fibromyxoid tumors of the adventitial dermis. Forme fruste of trichodiscoma? |
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| Authors: | C S McCalmont W L White J L Jorizzo |
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| Affiliation: | Department of Dermatology, Bowman Gray School of Medicine, Wake Forest University, Winston-Salem, North Carolina. |
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| Abstract: | A 36-year-old paraplegic man developed multiple giant fibromyxoid tumors surrounding a meningomyelocele scar that we believe are forme fruste of trichodiscomas. Histologic examination showed a papillated, slightly hyperplastic epidermis surrounding a delicate fibrovascular proliferation set in a stroma of loose fibrillar connective tissue and stellate fibroblasts. A melanocytic nevus was incorporated into one of the lesions. We believe that these giant lesions are connective tissue nevi of the adventitial dermis that comprise a new clinical variant of trichodiscoma. The potential significance of the relationship between these abortive trichodiscomas and abnormalities of the neural crest is discussed. |
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