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先天性内耳发育畸形的高分辨率CT表现
引用本文:张保隆,孙积宁,曹福志,于清霞,赵巍.先天性内耳发育畸形的高分辨率CT表现[J].中国优生与遗传杂志,2010(1):89-90.
作者姓名:张保隆  孙积宁  曹福志  于清霞  赵巍
作者单位:山东省潍坊市妇幼保健院放射科;山东省潍坊市人民医院放射科;
摘    要:目的探讨先天性内耳畸形的高分辨率CT表现。方法回顾性分析29例(46耳)婴幼儿先天性内耳发育畸形患者的CT表现,所有患者均做多层螺旋高分辨率CT横断面扫描及多平面重建,必要者利用容积再现技术对骨迷路进行三维重建。结果29例先天性内耳发育畸形患者双侧畸形者17例,单侧畸形者12例,内耳发育畸形共计46耳。具体分布如下:(1)Michel型(2耳),(2)耳蜗未发育(6耳),(3)共同腔畸形(5耳),(4)不完全分隔Ⅰ型(5耳),(5)不完全分隔Ⅱ型(传统Mondini型)(17耳),(6)耳蜗形态正常仅前庭及(或)半规管畸形(9耳),(7)单纯内耳道畸形(2耳)。结论高分辨率CT对先天性内耳骨迷路畸形具有重要的诊断价值,并可为人工耳蜗植入术适应证的选择提供重要依据。

关 键 词:内耳  畸形  高分辨率CT  体层摄影术

Appearance of high resolution CT in congenital inner ear malformations
ZHANG Bao - long,SUN Ji - ning,CAO Fu - zhi,YU Qing - xia,ZHAO Wei.Appearance of high resolution CT in congenital inner ear malformations[J].Chinese Journal of Birth Health & Heredity,2010(1):89-90.
Authors:ZHANG Bao - long  SUN Ji - ning  CAO Fu - zhi  YU Qing - xia  ZHAO Wei
Institution:1. Department of Radiology, Weifang Maternity and Child Care Hospital, Weifang Shandong 261011, China; 2. Department of Radiology, Weifang People's Hospital, Weifang Shandong 261041, China)
Abstract:Objective:To discuss the high resolution CT(HRCT) appearance of the congenital inner ear malformations.Methods:The HRCT appearance of 29 cases(46 ears) with congenital inner ear malformations were analyzed retrospectively.The axial images and multi-planar reconstruction were performed in each patient,and the 3D reconstruction of inner ear labrinth were done with volume rendering technique.Results:Seventeen patients were bilateral inner ear malformations among 29 patients.There are 46 ears with inner ear mal...
Keywords:Inner ear  Malformation  High-resolution CT  Tomography  
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