腔内治疗幼儿Budd-Chiari综合征1例并文献分析

目的总结血管腔内治疗I型幼儿布一加综合征（Budd—Chiari syndrome，BCS）的经验，并回顾相关文献。方法对1例BCS患儿行下腔静脉（IVC）造影，根据造影结果选择应用介入方法经皮腔内血管成形术治疗，即用超滑导丝硬头穿过下腔静脉阻塞狭窄部位，进行球囊扩张。结果①球囊扩张操作成功，无并发症发生。术后造影见残余狭窄≤30％，远期疗效有待进一步随访。②近年有关幼儿BCS的报道极少，静脉血管造影为诊断此病的金标准。结论介入治疗具有微创、安全、有效，术后并发症少，恢复快的优点，为治疗Ⅰ型幼儿BCS的首选方法。

Analysis of interventional endovascular treatment for a child with Budd-Chiari syndrome and literature review

Objective To summarize the experience of interventional therapy for a child with type I Budd-Chiari syndrome （BCS） and retrospectively review the related literature. Methods The child with BCS was examined with angiography of inferior vena cava （IVC）. The interventional procedures were based on the result of IVC phlebography. Percutaneous transluminal angioplasty（PTA） method was used in this case. The stenosis in the IVC was canalized and dilated with the hard tip of super-slide guide wire and balloon. Results （1）In this report, the balloon dilatation operative process was successful without any complications,and ≤30% stenosis was remained by angiography after PTA. Long-term effects need further follow-up. （2）In recent studies,reports about child type I Budd-Chiari syndrome were infrequent and the phlebography was the golden standard for definite diagnosis. Conclusion Interventional therapy for child type Ⅰ Budd-Chiari syndrome is less invasive, safe, effective, with less complications and fast recovery. It is the first choice of treatment for child type Ⅰ BCS.