Penetrating keratoplasty as a globe-saving procedure in fragile cornea

PURPOSE: To report a case of fragile cornea associated with osteogenesis imperfecta type I in which primary penetrating keratoplasty was done as a tectonic procedure. METHODS: A 6-year-old boy with osteogenesis imperfecta type I presented with a corneal laceration in his right eye following minor trauma. Since wound repair was not possible due to tissue loss, he underwent a primary penetrating keratoplasty. RESULTS: Postoperatively, the eye healed well without any wound leak. The boy had uneventful suture removal 10 weeks following surgery. CONCLUSION: Primary penetrating keratoplasty is a viable option to restore ocular integrity in fragile corneas following trauma when tissue loss precludes simple repair.