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EPSTEIN-BARR VIRUS-ASSOCIATED HAEMOPHAGOCYTIC SYNDROME IN A PATIENT WITH JUVENILE CHRONIC ARTHRITIS
Authors:DAVIES, S. V.   DEAN, J. D.   WARDROP, C. A. J.   JONES, J. H.
Affiliation:*Department of Haematology, University Hospital of Wales Cardiff
"{dagger}"Department of Medicine, University Hospital of Wales Cardiff
Abstract:We describe a case of reactive haemophagocytic syndrome (RHS)in a patient with previous polyarticular juvenile chronic arthritis(JCA). This is the first reported association of these conditionsand may be indicative of defective immunological responses toviral infections in this form of JCA. KEY WORDS: Epstein–Barr virus, Haemophagocytic syndrome, Juvenile chronic arthritis, Acquired coagulation disorder, Interferon-
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