EPSTEIN-BARR VIRUS-ASSOCIATED HAEMOPHAGOCYTIC SYNDROME IN A PATIENT WITH JUVENILE CHRONIC ARTHRITIS |
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Authors: | DAVIES, S. V. DEAN, J. D. WARDROP, C. A. J. JONES, J. H. |
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Affiliation: | *Department of Haematology, University Hospital of Wales Cardiff Department of Medicine, University Hospital of Wales Cardiff |
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Abstract: | We describe a case of reactive haemophagocytic syndrome (RHS)in a patient with previous polyarticular juvenile chronic arthritis(JCA). This is the first reported association of these conditionsand may be indicative of defective immunological responses toviral infections in this form of JCA. KEY WORDS: EpsteinBarr virus, Haemophagocytic syndrome, Juvenile chronic arthritis, Acquired coagulation disorder, Interferon- |
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