儿童肾脏少见肿瘤34例临床分析

目的：探讨儿童肾脏少见肿瘤的临床特点。方法回顾性分析2005年1月至2011年12月我们收治的34例肾脏少见肿瘤患儿临床资料。男性21例，女性13例。年龄4个月至17岁，平均年龄4.6岁。根据临床症状、辅助检查及治疗方法，分析儿童肾脏少见肿瘤的临床特点。结果腹部肿物、血尿、腹痛是常见的就诊原因。患儿术前均经超声及增强CT检查明确肾脏占位性病变，做出初步临床诊断。20例行瘤肾切除术，14例行保留肾单位的肿瘤切除术。术后根据病理类型，良性肿瘤予定期随访，恶性肿瘤予相应放化疗，目前23例获随访患儿均无瘤存活。结论儿童肾脏少见肿瘤的术前检查具有一定的特点，手术切除是治疗的首要选择，规范的综合治疗可以获得良好的预后。

Clinical characteristic of rare renal tumors in children

Objetive To summarize clinical characteristic of rare renal tumors in children. Methods The participants in this study were 34 patients who were admitted in the department of urology,Bei-jing Children’s Hospital,from January 2005 to December 201 1.21 were boys and 1 3 were girls. The age ranged from 4-month to 1 7-year （mean 4.6 years）. We analyzed the clinical characteristic of rare renal tumors in children in the aspect of clinical symptoms,examination and treatment. Results The most common symp-toms were abdomen mass,hematuria and abdominal pain. We made the initial diagnosis by ultrasound and en-hanced CT scan. 20 cases were undergone radical nephrectomy,and 1 4 cases were undergone partial nephrec-tomy. According to pathological types,the patients with benign tumors received regular follow-up,and the pa-tients with malignant tumors received chemotherapy and irradiation. 23 patients were followed up and they all survived without tumor at present. Conclusion There were some characteristics in the examinations of rare renal tumors.Surgical treatment was essential,and the comprehensive treatment could make the good prognosis.