Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery in Alagille Syndrome |
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| Authors: | Tara J. Lemoine DO Aditya K. Kaza MD Robert Gray MD Ronald W. Day MD Lloyd Y. Tani MD William Bradley Poss MD |
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| Affiliation: | 1. Division of Cardiothoracic Surgery, Department of Surgery, University of Utah School of Medicine, Salt Lake City, UT, USA;2. Division of Pediatric Cardiology, Department of Pediatrics and;3. Division of Pediatric Critical Care and |
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| Abstract: | Alagille syndrome is a dominantly inherited multisystem disorder involving multiple organs including the liver, heart, eyes, face, and skeleton. Congenital heart defects, the majority of which are right-sided, contribute significantly to the mortality of these patients. We report a patient with Alagille syndrome who presented with mitral valve regurgitation requiring valvuloplasty and subsequent mitral valve replacement. The patient was ultimately diagnosed with anomalous origin of the left coronary artery from the pulmonary artery and underwent successful reimplantation. |
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| Keywords: | ALCAPA Alagille Syndrome Mitral Valve |
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