Hirschsprung disease and anorectal malformation |
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| Affiliation: | 1. Department of Pediatrics, Case Western Reserve University and Rainbow Babies & Children''s Hospital, University Hospitals Case Medical Center, Cleveland, OH, United States;2. Department of Education, Cleveland State University, Cleveland, OH, United States;3. Departments of Psychology and of Special Education & Clinical Sciences, University of Oregon, Eugene, OR, United States;4. Developmental Cognitive Neuroscience Laboratory, University of Nebraska-Lincoln, Lincoln, NE, United States;5. Educational Consultant, Gates Mills, OH, United States;1. Department of General Pediatric Surgery, Robert Debre Children University Hospital, APHP, Paris, France;2. Paediatric Sleep Centre, Robert Debré Children University Hospital, APHP, EA 7334 REMES Paris-Diderot University, Paris, France;3. Department of Pediatric Pathology, Robert Debre Children University Hospital, APHP, Paris, France;4. Department of Intensive Care Unit, Robert Debre Children University Hospital, APHP, Paris, France;5. UMR1149 Inserm, Paris Diderot University, Paris, France;1. Department of Pediatric Surgery, Erasmus MC-Sophia Children''s Hospital, University Medical Center Rotterdam, Rotterdam, The Netherlands;2. Department for Health Evidence, Radboud University Nijmegen Medical Centre, Nijmegen, The Netherlands;3. Department of Pediatric Surgery, Colorectal Center for Children, Cincinnati Children''s Hospital Medical Center, University of Cincinnati College of Medicine, Cincinnati, OH, USA;4. Department of Surgery and Pediatric Surgery, Radboud University Nijmegen Medical Center, Nijmegen, The Netherlands |
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| Abstract: | Hirschsprung disease and Anorectal Malformations are congenital disorders presenting in neonates with distal intestinal obstruction. Hirschsprung disease is associated with a functional distal bowel obstruction resulting from the abnormal development of the enteric nervous system and ensuing aganglionosis of the distal gut. Anorectal Malformations comprise a spectrum of anatomical anomalies causing a mechanical bowel obstruction. Both conditions are frequently associated with congenital abnormalities/syndromes, which require careful assessment and evaluation. Surgical intervention is usually required for both conditions with careful preparation and meticulous technique. Long-term follow-up allows early identification and treatment of potentially debilitating symptoms, which include faecal incontinence. |
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