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Chiari畸形合并颅颈交界畸形的处理策略
引用本文:陈利锋,余新光,周定标,卜博,张远征,许百男.Chiari畸形合并颅颈交界畸形的处理策略[J].中国微侵袭神经外科杂志,2011,16(5):217-219.
作者姓名:陈利锋  余新光  周定标  卜博  张远征  许百男
作者单位:解放军总医院神经外科,北京,100853
摘    要:目的 探讨Chiari畸形合并颅颈交界畸形的临床特点及治疗方法.方法 回顾性分析56例Chiari畸形合并颅颈交界畸形的临床资料,其中合并颅底陷入35例,寰枕融合25例,颈椎分节不全6例.病人均行颅后窝减压硬脑膜扩大修补术,行小脑扁桃体部分切除术21例.固定方式采用钛缆固定和自体骨移植41例,C<,1>侧块~C<,2>椎弓根螺钉固定和自体骨移植15例.结果 术后发生颅内感染2例,脑脊液切口漏1例.55例随访6~60个月,平均42个月;植骨融合满意52例,钛缆固定和自体骨移植植骨未能融合3例;症状改善51例(92.7%),无变化4例(7.3%);随访期间无死亡病例.结论 Chiari畸形合并颅颈交界畸形应行颅颈交界关节稳定性检查及评估,对有潜在颅颈交界不稳定病人应行后路减压并枕颈植骨固定融合术,单纯后路减压可能加重颅颈交界不稳定,症状难以缓解甚至加重.

关 键 词:Arnold-Chiari畸形  颅颈交界畸形  关节融合术  减压术  外科

Treatment of Chiari malformation with craniocervical junction malformation
Chen Lifeng,Yu Xinguang,Zhou Dingbiao,Bu Bo,Zhang yuanzheng,Xu Bainan.Treatment of Chiari malformation with craniocervical junction malformation[J].Chinese Journal of Minimally Invasive Neurosurgery,2011,16(5):217-219.
Authors:Chen Lifeng  Yu Xinguang  Zhou Dingbiao  Bu Bo  Zhang yuanzheng  Xu Bainan
Institution:Chen Lifeng,Yu Xinguang,Zhou Dingbiao,Bu Bo,Zhang Yuanzheng,Xu Bainan Department of Neurosurgery,General Hospital of PLA,Beijing 100853,China
Abstract:Objective To investigate the clinical features and treatment of Chiari malformation complicated by craniocervical junction malformation.Methods Clinical data of 56 patients with Chiari malformation complicated by craniocervical junction malformation were retrospectively analyzed,including by basilar invagination in 35,by atlas assimilation in 25,by Klippel-Feil anomaly in 6.Posterior fossa decompression with expanded dural repair was performed in all the patients,including additional partial resection of th...
Keywords:Arnold-Chiari malformation  craniocervical junction malformation  arthrodesis  decompression  surgical  
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