孤立性巨细胞性肺动脉炎一例及文献复习

目的　了解孤立性巨细胞性肺动脉炎的临床及病理表现。方法　 1例右肺动脉完全堵塞患者 ,行右肺切除 ,标本取材后 ,石蜡包埋制片 ,苏木精 伊红及免疫组化染色。结合有关文献及本例患者的临床资料 ,对本病的临床及病理表现进行论述。结果　本病的病理表现主要为肺动脉管壁增厚、纤维组织及小血管增生 ,淋巴细胞 (主要为T淋巴细胞 )、浆细胞、组织细胞及少量多核巨细胞浸润 ,管腔血栓形成及机化 ,肺出血性梗死。结论　孤立性巨细胞性肺动脉炎是一种非常罕见的疾病 ,结合血管造影和病理检查可以确诊。

Isolated pulmonary giant cell arteritis:a case report and literature review

Objective To study the clinical and pathological characteristics of isolated pulmonary giant cell arteritis and its differential diagnosis. Methods The pathological data of a patient with isolated pulmonary giant cell arteritis were studied, and the literature was reviewed. Results The walls of the pulmonary artery and its major lobar branches were thickened, and the blood vessels were occluded by organizing thrombosis. The arterial wall was infiltrated by lymphocytes, mononuclear cells and some multinuclear giant cells. Conclusions Isolated pulmonary giant cell arteritis is a rare disease which can be definitely diagnosed by angiography and histopathology.