肝脏未分化性胚胎性肉瘤误诊分析

目的 加强对原发性肝脏未分化性胚胎性肉瘤的认识,提高其诊断率及生存率.方法 回顾分析我院2000年1月至2010年6月共13例肝脏未分化性胚胎性肉瘤临床资料,从临床及影像学角度,分析其误诊原因及随访结果.结果 13例患者中,男9例,女4例,最小年龄为8岁,最大年龄为63岁,中位年龄38岁.误诊为原发性肝癌6例,囊腺癌1...

MISDIAGNOSIS OF UNDIFFERENTIATED EMBRYONAL SARCOMA OF LIVER

Objective To deeply understand the undifferentiated embryonal sarcoma of liver（UES） and elevate its rate of correct diagnosis and survival rate.Methods In this study 13 patients under going hepatic resection were retrospectively studied from Jan 2000 to Jun 2010 in our hospital and we analyse the misdiagnosis and follow-up results of UES from the perspective of clinical and imaging.Results There are 9 males and 4 females in the group.Age at diagnosis of UES ranged from 8 to 63 years and the median age was 38 years.6 cases were misdiagnosed as hepatocellular carcinoma,1 cases as cystadenocarcinoma and 1 case as hepatoblastoma.5 cases were diagnosed as liver lesions.The main causes of misdiagnosis included atypical clinical and imaging features of UES,inexperienced recognition for UES,subjective assumptions and so on.There were no postoperative complications such as bleeding,jaundice,infection,hepatic encephalopathy and so on and the postoperative survival time ranged from 4 and 20 months and the median survival time was 7months.Conclusions Hepatic undifferentiated embryonal sarcoma is very difficult to diagnose correctly.Once UES is suspected,the operation should be performed as soon as possible and after operation,radiation therapy,chemotherapy and other adjuvant therapy should also received as early as possible which may improve the survival rate.