Malignant Peripheral Nerve Sheath Tumor of the Orbit: Case Report and Literature Review |
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Authors: | Mehmet D. Aydin Umran Yildirim Cemal Gundogdu Osman Dursun Hasan H. Uysal Mete Ozdikici |
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Affiliation: | Department of Neurosurgery, Medical Faculty, Ataturk University, Erzurum, Turkey. nmda21@hotmail.com |
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Abstract: | A 68-year-old woman with progressive visual loss and exophthalmos in her right eye had been operated on for a mass in her right calf 3 years earlier. Imaging showed a huge mass invading the orbital structures and temporal pole. The presumptive diagnosis was a malignant orbital tumor. The tumor was resected totally and eroded tissues such as the lateral rectus muscle and dural compartments were repaired. The histological diagnosis was a malignant peripheral nerve sheath tumor (MPNST). The patient recovered uneventfully and was discharged 8 days after surgery. Two years later she died from a liver tumor. Few MPNSTs involving the orbit have been reported. |
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