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Biliary drainage as treatment for allograft steatosis following liver transplantation for PFIC‐1 disease: A single‐center experience |
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| Authors: | Leina S. Alrabadi Raffaella A. Morotti Pamela L. Valentino Manuel I. Rodriguez‐Davalos Udeme D. Ekong Sukru H. Emre |
| Affiliation: | 1. Department of Pediatrics, Section of Pediatric Gastroenterology and Hepatology, Yale University School of Medicine, New Haven, CT, USA;2. Department of Pathology, Yale University School of Medicine, New Haven, CT, USA;3. Department of Surgery, Section of Transplantation and Immunology, Yale University School of Medicine, New Haven, CT, USA |
| Abstract: | Development of macrovesicular steatosis post–LT in patients with PFIC‐1 is increasingly being observed, with the etiology not fully understood. We highlight successful and effective EBD for reversal of allograft steatosis in 2 patients with PFIC‐1 disease and discuss our experience with internal biliary diversion in this patient population. |
| Keywords: | ATP8B1 cholestasis diarrhea disease recurrence graft dysfunction jaundice |