小儿腹膜后非嗜铬性副神经节瘤6例

目的 探讨腹膜后非嗜铬副神经节瘤（副节瘤）的诊断与治疗方法。方法 １９９２年２月～１９９８年８月收治６例腹膜后非嗜铬副神经节瘤，其中，男４例，妇女例。年龄５～１４岁，平均９．５岁。均采用手术切除治疗，３例取患侧１１肋间切口，２例１２肋缘下切口，１例经上腹切口。术中见肿瘤与腹主动脉、下腔静脉等粘连紧密，分离切除相当困难。１例下腔静脉撕裂行吻合术。病理诊断：良性副节瘤５例，恶生副节瘤１例。结果 所有病

Retroperitoneal nonchromaffin paraganglioma: a report of 6 cases

Objective To explore the diagnosis and treatment for retroperitoneal nonchromaffin paraganglioma. Methods From Feb.1992 to Aug.1998, 6 cases (male 4, female 2) with retroperitoneal nonchromaffin paraganglioma were treated. Their age ranged from 5 to 14 years (mean 9.5yrs ). The operation was performed through 11th intercostal incision (3), subcostal incision (2) and abdominal incision (1). The tumours were adherent to the abdominal aorta and inferior vena cava but resected completely except one case had a tear in inferior vena cava. Results The maximum diameter of the tumour was 6-7?cm. The pathological examination were benign in 5 and malignant in 1. The followed up of 4 cases from 1-4 years showed one died of tumor metastasis. Conclusions Surgical excision is the only therapeutic option. Adequate intravenous access, blood loss, sudden hypertension and avoid damaging adjacent main vessels are important to the resection of retroperitoneal nonchromaffin paraganglioma.