肾上腺脑白质营养不良MRI诊断 |
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引用本文: | 李彩霞,任翠萍,程敬亮,张勇,李丹,李建灵,李华丽,王娟. 肾上腺脑白质营养不良MRI诊断[J]. 实用放射学杂志, 2010, 26(3). DOI: 10.3969/j.issn.1002-1671.2010.03.005 |
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作者姓名: | 李彩霞 任翠萍 程敬亮 张勇 李丹 李建灵 李华丽 王娟 |
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作者单位: | 郑州大学第一附属医院磁共振室,河南,郑州,450052 |
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摘 要: | 目的 分析肾上腺脑白质营养不良(ALD)的影像图像特点,提高MRI对ALD诊断的准确性.方法 收集本院1993-2008年间经生化和临床证实的ALD共9例,所有病例均行MRI检查.结果 9例病人均表现为双侧对称性侧脑室三角区白质病变,呈T_1 WI低信号,T_2 WI高信号,经胼胝体压部相连,呈蝶翼状分布;其中1例仅累及枕叶, 6例累及顶枕叶,2例累及顶枕颞叶.8例累及胼胝体压部,5例累及丘脑后外部.2例增强扫描表现为病灶周边环状强化,脑干病灶亦强化.结论 MRI能准确反映ALD病变和病程.
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关 键 词: | 脑 肾上腺脑白质营养不良 磁共振成像 |
Adrenoleukodystrophy: MR Imaging Diagnosis |
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Abstract: | Objective To analyse imaging (CT and MR imaging) features of adrenoleukodystrophy(ALD). Methods 9 cases with ALD proved both biochemically and clinically from 1993 to 2008 in our hospital were reviewed. All of them underwent MR examinations. Results All of the cases showed a bilaterial symmetrical changes in the posterior periventricular white matter. The lesions were low signal intensity on T_1 WI and high signal intensity on T_2 WI, which appeared as a butterfly pattern with infiltration of the corpus callosum splenium. The lesions involved the occipital lobe in one, the occipitopariet al lobe in 6 and the occipitoparietotem-poral lobe in 2 respectively. The brain stem involved in 8 patients,the lateral posterior part of the thalamus involved in 5. The ring like-enhancement of bilaterial occipital lobe was found in two patients with post contrast studies. Conclusion MRI may correctly demonstrate the lesions and progression of ALD. |
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Keywords: | brain adrenoleukodystrophy MR imaging |
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