腹膜后淋巴管瘤的诊断与治疗

目的总结腹膜后淋巴管瘤的临床及影像学特点，提高对该病的诊治水平。方法回顾性分析经病理证实的11例腹膜后淋巴管瘤的临床和影像学资料。其中男7例，女4例，年龄6—57岁，平均42岁。患者均无特征性临床表现，B超和CT均表现为边缘光整的囊性肿块。其中单房囊肿7例，多房囊肿4例。术前仅有1例患者经B超引导下穿刺抽液而确诊。结果11例均行手术完整切除肿瘤，其中9例行开放手术，2例行后腹腔镜下切除肿瘤。全组均病理证实为（腹膜后）淋巴管瘤，随访8个月～12年未见复发。结论腹膜后淋巴管瘤由于临床上无特异性表现而易漏诊和误诊，诊断主要依靠影像学检查，细针穿刺有助于提高腹膜后淋巴瘤的诊断，手术完整切除是治疗首选。

The diagnosis and treatment of retroperitoneal iymphangioma

Objective To study the clinical and imaging features of retroperitoneal lymphangioma and improve the level of the diagnosis and treatment of the disease. Methods The clinical and imaging data of 11 patients （7 males and 4 femals） with retroperitoneal lymphangioma proved pathologically were analyzed retrospectively. Their age ranged from 6 to 57 years with a mean of 42 years. All patients presented no special clinical manifestation. Uhrasonography and CT scan showed smoothly margined cystic masses. Seven cases were unilocular and 4 cases were muhilocular. Preoperative definite diagnosis was made in only 1 case by uhrasonography - guided percutaneous catheter drainage of the lymphangioma. Results All the patients were performed complex excision. Open excision was carried out in 9 cases and retroperitoneal laparoscopic excision in 2 cases. The diagnosis of all cases was confirmed by pathologic studies. There was no recurrence during the follow - up 8 mouths to 12 years. Conclusions Retroperitoheal lymphangioma is often delayed or missed diagnosis due to its unspecific clinical presentation. The diagnosis depends on image examinations, fine noodle aspiration is helpful to its diagnosis. Complete excision is the first choice in the treatment.