逆行胰胆管造影诊断胰胆系罕见、少见疾病的价值

目的：明确国人胰胆系罕见、少见疾病与其他胰胆疾病的关系，提高胰胆系疾病的检出率。方法：分析1984年5月－2001年1月间成功行逆行胰胆管造影1061例，其中先天性胆管囊性扩张症、胰胆管合流异常、乳头旁憩室等胰胆系罕少疾病160例。结果：胰胆系罕少疾病占15％（160／1061）, 单病种的检出占0．09％－6．22％。胰胆系罕少疾病中约60％合并其他胰胆疾病。结论：胰胆系罕少疾病同时合并其他胰胆疾病的发病率高，应引起临床重视。

The clinical significance of ERCP in the diagnosis of rare cholangio-pancreatic disease

Objective::To evaluate the relationship between the diagnosis rate of rare cholangio pancreatic disease and other cholangio pancreatic disease.Methods:160 cases of congenital choledochal cyst,malfusion of the pancreatobiliary ducts, periampullary diverticulum and other rare cases were diagnosed among 1 061 cases with endoscopic retrograde cholangio pancreatography in the hospital from May 1984 to Jan.2001.Results:The diagnosis rate of rare cholangio pancreatic disease is 15%(160/1061) ,the diagnosis rate of each rare disease is 0.09% 6.22% and 60% rare cholangio pancreatic disease complicated with other cholangio pancreatic disease.Conclusion:There is a high incidence of the rare cases complicated with other cholangio pancreatic disease simutaneously,which should be paid attention to in clinical practice.