大前庭导水管综合征的临床特点

目的进一步认识前庭导水管综合征的临床特点,减少误诊,及时治疗。方法13例患者分别作了听力学检查和高分辨率颞骨横断位CT扫描,其中6例作了內听道MRI扫描,具体测量相关数据。结果13例全部有严重的听力损失,4例听力有波动性,3例有头颅外伤史。在CT图像上,12例双侧和1例单侧有前庭导水管扩大。MRI图像上,5例双侧、1例单侧内淋巴管和内淋巴囊均有扩大。结论该病的诊断应综合分析临床资料及影像学图像,才能做到早期诊断和及时治疗。

Clinical characteristics of patients with large vestibular aqueduct syndrome

Objective To further study the clinical characteristics of large vestibular aqueduct syndrome, decrease the rate of misdiagnosis and enable timely treatment. Methods Thirteen patients with large vestibular aqueduct underwent hearing examination and high-resolution CT scan, among them six patients took MR examinations and three patients had head trauma before hearing loss. The width of vestibular aqueduct (on CT scans) was measured at the midpoint of the distal limb. Results All the cases had grave sensorineural hearing loss, of whom, four were diagnosed with fluctuating hearing. Most of the cases examined were found with pathological changes in vestibular aqueduct enlargement after high resolution CT scan and MRI in inner ear. Conclusion To get early diagnosis and prompt therapy, clinical data and images should be analyzed aggregately.