复发性多软骨炎7例报告

目的探讨复发性多软骨炎的临床特点和诊疗方法。方法回顾性分析7例复发性多软骨炎患者的临床特点、治疗结果并复习相关文献。结果7例患者中侵犯呼吸道5例,耳4例,鼻3例,关节2例,眼1例,耳蜗和前庭1例。平均漏诊或误诊时间为2.1年。均给予糖皮质激素治疗,其中3例因气道狭窄行气管支架置入术,患者症状明显缓解。结论复发性多软骨炎临床表现复杂多样,极易误诊、漏诊,临床需提高对该病的认识。糖皮质激素治疗疗效明显,合并气道狭窄的可行纤支镜引导下气管支架置入术。

Clinical Features and Treatment of Relapsing Polychondritis

Objective To explore the clinical features,diagnosis and treatment of relapsing polychondritis（RP）.Methods Seven patients with RP were retrospectively analyzed and related literature was reviewed.Results The sites involved included airway in 5,auricle in 4,nose in 3,joint in 2,eye in 1 and inner ear in 1 patient（s）.The average time of misdiagnosis or missed diagnosis was 2.1 years.All the patients were treated with glucocorticosteroids and 3 patients received airway stenting for their airway stenosis.They were all alleviated after treatment.Conclusion The clinical manifestation of RP is multiple and patients with RP tend to be misdiagnosed or missed.On the basis of glucocorticosteroid treatment,patients with airway stenosis should receive airway stenting.